Spontaneous pneumomediastinum and dermatomyositis may be a not so rare association: report of a case and review of the literature
Identifieur interne : 001C57 ( Main/Exploration ); précédent : 001C56; suivant : 001C58Spontaneous pneumomediastinum and dermatomyositis may be a not so rare association: report of a case and review of the literature
Auteurs : Fabricio De Souza Neves [Brésil] ; Samuel Katsuyuki Shinjo [Brésil] ; Jozélio Freire Carvalho [Brésil] ; Maurício Levy-Neto [Brésil] ; Cláudia Tereza Lobato Borges [Brésil]Source :
- Clinical Rheumatology [ 0770-3198 ] ; 2007-01-01.
English descriptors
- KwdEn :
Abstract
Abstract: One patient with dermatomyositis (DM) who developed spontaneous pneumomediastinum (SPnM) is described. A review of 15 previously reported cases shows that this is a complication of DM but not of polymyositis. It occurs in young patients with recent onset of disease characterized by cutaneous vasculopathy, and patients treated with immunosuppressive drugs have, in general, better outcomes. We suggest that the onset of SPnM in DM patients must alert to possible vasculitic activity and that immunosuppressive agents with progressive tapering of corticosteroids are part of the most reasonable approach in these cases.
Url:
DOI: 10.1007/s10067-005-0109-x
Affiliations:
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Le document en format XML
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<front><div type="abstract" xml:lang="en">Abstract: One patient with dermatomyositis (DM) who developed spontaneous pneumomediastinum (SPnM) is described. A review of 15 previously reported cases shows that this is a complication of DM but not of polymyositis. It occurs in young patients with recent onset of disease characterized by cutaneous vasculopathy, and patients treated with immunosuppressive drugs have, in general, better outcomes. We suggest that the onset of SPnM in DM patients must alert to possible vasculitic activity and that immunosuppressive agents with progressive tapering of corticosteroids are part of the most reasonable approach in these cases.</div>
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<name sortKey="Carvalho, Jozelio Freire" sort="Carvalho, Jozelio Freire" uniqKey="Carvalho J" first="Jozélio Freire" last="Carvalho">Jozélio Freire Carvalho</name>
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